Idiopathic Pulmonary Fibrosis

Overview

Idiopathic pulmonary fibrosis (IPF) is the most common idiopathic interstitial pneumonia, a chronic progressive fibrosing disease of unknown cause confined to the lungs. Widespread fibrosis thickens the lung tissue and irreversibly impairs oxygen exchange, making it a fatal respiratory disease with generally poor prognosis.

Symptoms

• Progressive shortness of breath
• Dry cough
• Fatigue
• Clubbing of fingers

Treatment

There is no cure at present; antifibrotic drugs can slow disease progression, and severe cases are considered for long-term oxygen therapy and lung transplantation.

Dietary advice

Balanced nutrition, small frequent meals to reduce breathing effort, and consistent smoking cessation.